The epidemiology of PAH varies between studies and depends upon the population in question and the aetiology of the condition. The UK National Audit on Pulmonary Hypertension 2012 showed the prevalence of PAH in Scotland to be 48.5 cases per million population.
Throughout the UK, the audit showed the proportion of patients in different subcategories of PAH to be as below:
In conditions associated with PAH, the prevalence of PH varies widely, illustrated in the table below.
Condition | % with PAH |
Systemic sclerosis | 12 |
Congenital heart disease | 15-29 |
Portal hypertension | 2 |
HIV | 0.5 |